ARHP - Helps,C.R.; Fisher,A.V.; Harbour,D.A.; O'Neill,D.H.; Knight,A.C. - Transfer of spinal cord material to subsequent bovine carcasses at splitting - Journal of Food Protection 2004 Sep; 67(9): 1921-6
ANTP - Helps,C.R.; Hindell,P.; Hillman,T.J.; Fisher,A.V.; Anil,M.H.; Knight,A.C.; Whyte,R.T.; O'Niell,D.H.; Knowles,T.G.; Harbour,D.A. - Contamination of beef carcasses by spinal cord tissue during splitting - Food Control 2002; 13: 417-23
APIT - Knight,J. - Academy calls for improved tests to beat prion disease - Nature 2003 Nov 20; 426(6964): 216
AGPH - Knight,J. - Ranches blamed over spread of mad deer - Nature 2002 Apr 11; 416(6881): 569-70
AUKX - Knight,J. - Which prion - New Scientist 1998; 160(2154): 13
AGPI - Knight,J.A. - Advances in the analysis of cerebrospinal fluid - Annals of Clinical and Laboratory Science 1997 Mar-Apr; 27(2): 93-104
AVUP - Green,A.J.E.; Sanchez-Juan,P.; Ladogana,A.; Cuadrado Corrales,N.; Sanchez-Valle,R.; Mitrova,E.; Stoeck,K.; Sklaviadis,T.K.; Kulczycki,J.; Heinemann,U.; Hess,K.; Slivarichova,D.; Saiz,A.; Calero,M.; Mellina,V.; Knight,R.; van Duijn,C.M.; Zerr,I. - CSF analysis in patients with sporadic CJD and other transmissible spongiform encephalopathies - European Journal of Neurology 2007 Feb; 14(2): 121-4
AWZE - Hesketh,S.; Sassoon,J.; Knight,R.; Hopkins,J.; Brown,D.R. - Elevated manganese levels in blood and central nervous system occur before onset of clinical signs in scrapie and bovine spongiform encephalopathy - Journal of Animal Science 2007 Jun; 85(6): 1596-609
AXQA - Knight,R.; Stewart,L.; Rydzewska,L.; Keogh,G.; Chalmers,I.; Firkins,L.; Walker,S. - A Systematic Review of Therapeutic Interventions for Human Prion Disease - International Conference - Prion 2007 (26.-28.9.2007) Edinburgh International Conference Centre, Edinburgh, Scotland, UK - Book of Abstracts: Oral Abstracts FC5.4
AVBT - Sanchez-Juan,P.; Green,A.; Ladogana,A.; Cuadrado Corrales,N.; Saanchez-Valle,R.; Mitrovaa,E.; Stoeck,K.; Sklaviadis,T.K.; Kulczycki,J.; Hess,K.; Bodemer,M.; Slivarichova,D.; Saiz,A.; Calero,M.; Ingrosso,L.; Knight,R.; Janssens,A.C.; van Duijn,C.M.; Zerr,I. - CSF tests in the differential diagnosis of Creutzfeldt-Jakob disease - Neurology 2006 Aug 22; 67(4): 637-43
ALQI - Thackray,A.M.; Knight,R.; Haswell,S.J.; Bujdoso,R.; Brown,D.R. - Metal imbalance and compromised antioxidant function are early changes in prion disease - Biochemical Journal 2002 Feb 15; 362(1): 253-8
ANOS - Andrews,N.J.; Farrington,C.P.; Ward,H.J.T.; Cousens,S.N.; Smith,P.G.; Molesworth,A.M.; Knight,R.S.G.; Ironside,J.W.; Will,R.G. - Deaths from variant Creutzfeldt-Jakob disease in the UK - Lancet 2003 Mar 1; 361(9359): 751-2
AAHH - Andrews,N.J.; Farrington,C.P.; Cousens,S.N.; Smith,P.G.; Ward,H.J.T.; Knight,R.S.G.; Ironside,J.W.; Will,R.G. - Incidence of variant Creutzfeldt-Jakob disease in the UK - Lancet 2000 Aug 5; 356(9228): 481-2
ACPL - Choe,L.H.; Green,A.; Knight,R.S.G.; Thompson,E.J.; Lee,K.H. - Apolipoprotein E and other cerebrospinal fluid proteins differentiate ante mortem variant Creutzfeldt-Jakob disease from ante mortem sporadic Creutzfeldt-Jakob disease - Electrophoresis 2002 Jul; 23(14): 2242-6
APGK - Collie,D.A.; Summers,D.M.; Sellar,R.J.; Ironside,J.W.; Cooper,S.A.; Zeidler,M.; Knight,R.S.G.; Will,R.G. - Diagnosing variant Creutzfeldt-Jakob disease with the pulvinar sign: MR imaging findings in 86 neuropathologically confirmed cases. - AJNR. American Journal of Neuroradiology 2003 Sep; 24(8): 1560-9
ACTI - Collie,D.A.; Sellar,R.J.; Zeidler,M.; Colchester,A.F.C.; Knight,R.S.G.; Will,R.G. - MRI of Creutzfeldt-Jakob disease: imaging features and recommended MRI protocol. - Clinical Radiology 2001 Sep; 56(9): 726-39
AVKT - Cooper,S.A.; Murray,K.L.; Heath,C.A.; Will,R.G.; Knight,R.S.G. - Sporadic Creutzfeldt-Jakob disease with cerebellar ataxia at onset in the UK - Journal of Neurology, Neurosurgery and Psychiatry 2006 Nov; 77(11): 1273-5
ATCF - Cooper,S.A.; Murray,K.L.; Heath,C.A.; Will,R.G.; Knight,R.S.G. - Isolated visual symptoms at onset in sporadic Creutzfeldt-Jakob disease: the clinical phenotype of the "Heidenhain variant". - The British Journal of Ophthalmology 2005 Oct; 89(10): 1341-2
ACXD - Cousens,S.N.; Smith,P.G.; Ward,H.J.T.; Everington,D.; Knight,R.S.G.; Zeidler,M.; Stewart,G.; Smith-Bathgate,E.A.; Macleod,M.A.; Mackenzie,J.; Will,R.G. - Geographical distribution of variant Creutzfeldt-Jakob disease in Great Britain, 1994-2000 - Lancet 2001 Mar 31; 357(9261): 1002-7
ACXE - Cousens,S.N.; Linsell,L.; Smith,P.G.; Chandrakumar,M.; Wilesmith,J.W.; Knight,R.S.G.; Zeidler,M.; Stewart,G.; Will,R.G. - Geographical distribution of variant CJD in the UK (excluding Northern Ireland) - Lancet 1999 Jan 2; 353(9146): 18-21
ACXH - Cousens,S.N.; Harries-Jones,R.; Knight,R.S.G.; Will,R.G.; Smith,P.G.; Matthews,W.B. - Geographical distribution of cases of Creutzfeldt-Jakob disease in England and Wales 1970-84 - Journal of Neurology, Neurosurgery and Psychiatry 1990 Jun; 53(6): 459-65
ADCM - de Silva,R.N.; Findlay,C.; Awad,I.; Harries-Jones,R.; Knight,R.S.G.; Will,R. - Creutzfeldt-Jakob disease in the elderly - Postgraduate Medical Journal 1997 Sep; 73(863): 557-9
ADUW - Esmonde,T.F.G.; Will,R.G.; Slattery,J.M.; Knight,R.S.G.; Harries-Jones,R.; de Silva,R.N.; Matthews,W.B. - Creutzfeldt-Jakob disease and blood transfusion - Lancet 1993 Jan 23; 341(8839): 205-7
AUAK - Goodall,C.A.; Head,M.W.; Everington,D.; Ironside,J.W.; Knight,R.S.G.; Green,A.J.E. - Raised CSF phospho-tau concentrations in variant Creutzfeldt-Jakob disease: diagnostic and pathological implications. - Journal of Neurology, Neurosurgery and Psychiatry 2006 Jan; 77(1): 89-91
AEVU - Green,A.J.E.; Ramljak,S.; Müller,W.E.G.; Knight,R.S.G.; Schröder,H.C. - 14-3-3 in the cerebrospinal fluid of patients with variant and sporadic Creutzfeldt-Jakob disease measured using capture assay able to detect low levels of 14-3-3 protein - Neuroscience Letters 2002 May 10; 324(1): 57-60
AEVV - Green,A.J.E.; Thompson,E.J.; Stewart,G.E.; Zeidler,M.; McKenzie,J.M.; Macleod,M.A.; Ironside,J.W.; Will,R.G.; Knight,R.S.G. - Use of 14-3-3 and other brain-specific proteins in CSF in the diagnosis of variant Creutzfeldt-Jakob disease - Journal of Neurology, Neurosurgery and Psychiatry 2001 Jun; 70(6): 744-8
AEVW - Green,A.J.E.; Knight,R.S.G.; Macleod,M.A.; Lowman,A.; Will,R.G. - Misleading results with the 14-3-3 assay for the diagnosis of Creutzfeldt-Jakob disease - Neurology 2001 Apr 10; 56(7): 986-7
AFDL - Harries-Jones,R.; Knight,R.S.G.; Will,R.G.; Cousens,S.N.; Smith,P.G.; Matthews,W.B. - Creutzfeldt-Jakob disease in England and Wales, 1980-1984: a case-control study of potential risk factors. - Journal of Neurology, Neurosurgery and Psychiatry 1988 Sep; 51(9): 1113-9
AUAQ - Head,M.W.; Kouverianou,E.; Taylor,L.; Green,A.; Knight,R.S.G. - Evaluation of urinary PrPsc as a diagnostic test for sporadic, variant, and familial CJD - Neurology 2005 May 24; 64(10): 1794-6
AQSX - Head,M.W.; Bunn,T.J.R.; Bishop,M.T.; McLoughlin,V.; Lowrie,S.; McKimmie,C.S.; Williams,M.C.; McCardle,L.; Mackenzie,J.; Knight,R.S.G.; Will,R.G.; Ironside,J.W. - Prion protein heterogeneity in sporadic but not variant Creutzfeldt-Jakob disease: UK cases 1991-2002. - Annals of Neurology 2004 Jun; 55(6): 851-9
AOTV - Head,M.W.; Bunn,T.J.R.; Bishop,M.T.; Knight,R.S.G.; Will,R.G.; Ironside,J.W. - Heterogeneity in the abnormal prion protein isoforms found in the brains of sporadic but not variant Creutzfeldt-Jakob disease patients - International Conference - Prion diseases: from basic research to intervention concepts - TSE-Forum, 08.10.-10.10.2003, Gasteig, München - Poster session - DG-03
AUTY - Heath,C.A.; Barker,R.A.; Esmonde,T.F.G.; Harvey,P.; Roberts,R.; Trend,P.; Head,M.W.; Smith,C.; Bell,J.E.; Ironside,J.W.; Will,R.G.; Knight,R.S.G. - Dura mater-associated Creutzfeldt-Jakob disease: experience from surveillance in the UK. - Journal of Neurology, Neurosurgery and Psychiatry 2006 Jul; 77(7): 880-2
AFHS - Henry,C.; Knight,R.S.G. - Clinical features of variant Creutzfeldt-Jakob disease - Reviews in Medical Virology 2002 May-Jun; 12(3): 143-50
AOUJ - Ironside,J.W.; Head,M.W.; McCardle,L.; Ritchie,D.; Will,R.G.; Ward,H.J.T.; Knight,R.S.G. - Pathological approaches to study the epidemiology of variant CJD - International Conference - Prion diseases: from basic research to intervention concepts - TSE-Forum, 08.10.-10.10.2003, Gasteig, München - Oral sessions OS-02
AFVA - Ironside,J.W.; Head,M.W.; McCardle,L.; Knight,R.S.G. - Neuropathology of variant Creutzfeldt-Jakob disease - Acta Neurobiologiae Experimentalis 2002; 62(3): 175-82
AFVJ - Ironside,J.W.; Knight,R.S.G.; Will,R.G.; Smith,P.G.; Cousens,S.N. - New variant Creutzfeldt-Jakob disease is more common in Britain than elsewhere - British Medical Journal 1998 Aug 1; 317(7154): 352
AUYJ - Knight,R.S.G. - Creutzfeldt-Jakob disease: a rare cause of dementia in elderly persons. - Clinical Infectious Diseases 2006 Aug 1; 43(3): 340-6
AVAZ - Knight,R.S.G.; Stanley,S.; Wong,M.; Dolan,G. - Hemophilia therapy and blood-borne pathogen risk - Seminars in Thrombosis and Hemostasis 2006 Jun; 32 Suppl 2: 3-9
AQYR - Knight,R.S.G. - Prion diseases - Vox Sanguinis 2004 Jul; 87 Suppl1: 104-6
AQLQ - Knight,R.S.G.; Brazier,M.W.; Collins,S.J. - Human prion diseases: cause, clinical and diagnostic aspects. - Contributions to Microbiology 2004; 11: 72-97
AQDG - Knight,R.S.G.; Will,R.G. - Prion diseases - Journal of Neurology, Neurosurgery and Psychiatry 2004 Mar; 75 Suppl 1: i36-42
APRE - Knight,R.S.G. - Variant CJD: the present position and future possibilities. - International Journal of Pediatric Otorhinolaryngology 2003 Dec; 67 Suppl 1: S81-4
ANEX - Knight,R.S.G. - CJD: are there distinct neuropsychological features? - Journal of Neurology, Neurosurgery and Psychiatry 2002 Dec; 73(6): 613-4
ANIU - Knight,R.S.G. - Epidemiology of variant CJD - Developments in Biologicals 2002; 108: 87-92
AGPJ - Knight,R.S.G. - Creutzfeldt-Jakob disease: a protein disease. - Proteomics 2001 Jun; 1(6): 763-6
AGPK - Knight,R.S.G.; Collins,S. - Human prion diseases: cause, clinical and diagnostic aspects. - Contributions to Microbiology 2001; 7: 68-92
AGPL - Knight,R.S.G. - The relationship between new variant Creutzfeldt-Jakob disease and bovine spongiform encephalopathy - Vox Sanguinis 1999; 76(4): 203-8
AGPM - Knight,R.S.G. - The diagnosis of prion diseases - Parasitology 1998; 117 Suppl: S3-11
AGPN - Knight,R.S.G. - Creutzfeldt-Jakob disease: clinical features, epidemiology and tests. - Electrophoresis 1998 Jun; 19(8-9): 1306-10
AGPO - Knight,R.S.G.; Stewart,G. - The new variant form of Creutzfeldt-Jakob disease - FEMS Immunology and Medical Microbiology 1998 Jun; 21(2): 97-100
AGPP - Knight,R.S.G. - Creutzfeldt-Jakob disease - British Journal of Hospital Medicine 1989 Feb; 41(2): 165-6, 168-71
AUBF - Kovacs,G.G.; Puopolo,M.; Ladogana,A.; Pocchiari,M.; Budka,H.; van Duijn,C.M.; Collins,S.J.; Boyd,A.; Giulivi,A.; Coulthart,M.B.; Delasnerie-Laupretre,N.; Brandel,J.P.; Zerr,I.; Kretzschmar,H.A.; de Pedro Cuesta,J.; Calero-Lara,M.; Glatzel,M.; Aguzzi,A.; Bishop,M.T.; Knight,R.S.G.; Belay,G.; Will,R.; Mitrova,E. - EUROCJD. - Genetic prion disease: the EUROCJD experience. - Human Genetics 2005 Nov; 118(2): 166-74
AGTD - Kovacs,G.G.; Trabattoni,G.; Hainfellner,J.A.; Ironside,J.W.; Knight,R.S.G.; Budka,H. - Mutations of the prion protein gene - Phenotypic spectrum - Journal of Neurology. Zeitschrift für Neurologie 2002 Nov; 249(11): 1567-82
ATVU - Ladogana,A.; Puopolo,M.; Croes,E.A.; Budka,H.; Jarius,C.; Collins,S.J.; Klug,G.M.; Sutcliffe,T.; Giulivi,A.; Alperovitch,A.; Delasnerie-Laupretre,N.; Brandel,J.P.; Poser,S.; Kretzschmar,H.A.; Rietveld,I.; Mitrova,E.; de Pedro Cuesta,J.; Martinez-Martin,P.; Glatzel,M.; Aguzzi,A.; Knight,R.S.G.; Ward,H.J.T.; Pocchiari,M.; van Duijn,C.M.; Will,R.G.; Zerr,I. - Mortality from Creutzfeldt-Jakob disease and related disorders in Europe, Australia, and Canada - Neurology 2005 May 10; 64(9): 1586-91
ARLR - Linsell,L.; Cousens,S.N.; Smith,P.G.; Knight,R.S.G.; Zeidler,M.; Stewart,G.; de Silva,R.; Esmonde,T.F.G.; Ward,H.J.T.; Will,R.G. - A case-control study of sporadic Creutzfeldt-Jakob disease in the United Kingdom: analysis of clustering. - Neurology 2004 Dec 14; 63(11): 2077-83
APWY - Llewelyn,C.A.; Hewitt,P.E.; Knight,R.S.G.; Amar,K.; Cousens,S.N.; Mackenzie,J.; Will,R.G. - Possible transmission of variant Creutzfeldt-Jakob disease by blood transfusion - Lancet 2004 Feb 7; 363(9407): 417-21
AHRP - Macleod,M.A.; Stewart,G.E.; Zeidler,M.; Will,R.; Knight,R.S.G. - Sensory features of variant Creutzfeldt-Jakob disease - Journal of Neurology. Zeitschrift für Neurologie 2002 Jun; 249(6): 706-11
AHSR - Majeed,A.; Lehmann,P.; Kirby,L.; Knight,R.S.G.; Coleman,M.P. - Extent of misclassification of death from Creutzfeldt-Jakob disease in England 1979-96: retrospective examination of clinical records. - British Medical Journal 2000 Jan 15; 320(7228): 145-7
AIKA - Minghetti,L.; Cardone,F.; Greco,A.; Puopolo,M.; Levi,G.; Green,A.J.E.; Knight,R.S.G.; Pocchiari,M. - Increased CSF levels of prostaglandin E(2) in variant Creutzfeldt-Jakob disease - Neurology 2002 Jan 8; 58(1): 127-9
APKM - Nurmi,M.H.; Bishop,M.T.; Strain,L.; Brett,F.M.; McGuigan,C.; Hutchison,M.; Farrell,M.A.; Tilvis,R.; Erkkila,S.; Simell,O.; Knight,R.S.G.; Haltia,M. - The normal population distribution of PRNP codon 129 polymorphism - Acta Neurologica Scandinavica 2003 Nov; 108(5): 374-8
AQOH - Sanchez-Juan,P.; Ward,H.J.T.; de Silva,R.; Knight,R.S.G.; Will,R.G. - Ophthalmic surgery and Creutzfeldt-Jakob disease - The British Journal of Ophthalmology 2004 Apr; 88(4): 446-9
ALBQ - Spencer,M.D.; Knight,R.S.G.; Will,R.G. - First hundred cases of variant Creutzfeldt-Jakob disease: retrospective case note review of early psychiatric and neurological features. - British Medical Journal 2002 Jun 22; 324(7352): 1479-82
ALGJ - Summers,D.M.; Collie,D.A.; Sellar,R.J.; Zeidler,M.; Knight,R.S.G.; Will,R.G.; Ironside,J.W. - The pulvinar sign and diagnosis of Creutzfeldt-Jakob disease - Neurology 2002 Sep 24; 59(6): 962; discussion 962
AXYL - Ward,H.J.T.; Sneddon,J.; Reilly,J.; Chow,Y.; Soldan,K.; Knight,R.S.G.; Will,R.G. - Variant CJD: A Review of Individuals Designated "at Risk" due to Exposure through Medical Procedures or Blood Transfusion - International Conference - Prion 2007 (26.-28.9.2007) Edinburgh International Conference Centre, Edinburgh, Scotland, UK - Book of Abstracts: Epidemiology, Risk Assessment and Transmission P04.13
AWQE - Ward,H.J.T.; Everington,D.; Cousens,S.N.; Smith-Bathgate,B.; Gillies,M.; Murray,K.; Knight,R.S.G.; Smith,P.G.; Will,R.G. - Secondary transmission of sporadic Creutzfeldt-Jakob disease via surgery in the UK? - International Conference - Prion 2006: Strategies, advances and trends towards protection of society - 3.10.-6.10.2006, Torino, Italy, Lingotto Conference Centre - Poster sessions EPI-26
ATES - Ward,H.J.T.; Everington,D.; Cousens,S.N.; Smith-Bathgate,B.; Leitch,M.; Cooper,S.A.; Heath,C.; Knight,R.S.G.; Smith,P.G.; Will,R.G. - Risk factors for variant Creutzfeldt-Jakob disease: a case-control study. - Annals of Neurology 2006 Jan; 59(1): 111-20
APAF - Ward,H.J.T.; Sanchez-Jaun,P.; Smith,A.J.; Everington,D.; Cooper,S.A.; Heath,C.; Knight,R.S.G.; Will,R.G. - Secondary transmission of variant Creutzfeldt-Jakob Disease (vCJD)? - International Conference - Prion diseases: from basic research to intervention concepts - TSE-Forum, 08.10.-10.10.2003, Gasteig, München - Poster session - BR-61
AVEY - Whittle,I.R.; Knight,R.S.G.; Will,R.G. - Unsuccessful intraventricular pentosan polysulphate treatment of variant Creutzfeldt-Jakob disease - Acta Neurochirurgica 2006 Jun; 148(6): 677-9; discussion 679
AAHL - Wiersma,S.; Cooper,S.A.; Knight,R.S.G.; Kennedy,A.M.; Joiner,S.; Belay,E.D.; Schonberger,L.B. - Probable variant Creutzfeldt-Jakob disease in a U.S. resident - Florida, 2002. - MMWR. Morbidity and Mortality Weekly Report 2002 Oct 18; 51(41): 927-9
ATGI - Will,R.G.; Knight,R.S.G.; Ward,H.J.T. - Variant CJD: past, present and future - International Conference - Prion 2005: Between fundamentals and society's needs - 19.10.-21.10.2005, Congress Center Düsseldorf - Oral sessions ORAL-39
AMNQ - Will,R.G.; Knight,R.S.G.; Ward,H.J.T.; Ironside,J.W. - vCJD: the epidemic that never was. New variant Creutzfeldt-Jakob disease: the critique that never was. - British Medical Journal 2002 Jul 13; 325(7355): 102
AMNU - Will,R.G.; Zeidler,M.; Stewart,G.E.; Macleod,M.A.; Ironside,J.W.; Cousens,S.N.; Mackenzie,J.; Estibeiro,K.; Green,A.J.E.; Knight,R.S.G. - Diagnosis of new variant Creutzfeldt-Jakob disease - Annals of Neurology 2000 May; 47(5): 575-82
AMNX - Will,R.G.; Cousens,S.N.; Farrington,C.P.; Smith,P.G.; Knight,R.S.G.; Ironside,J.W. - Deaths from variant Creutzfeldt-Jakob disease - Lancet 1999 Mar 20; 353(9157): 979
AMOD - Will,R.G.; Knight,R.S.G.; Zeidler,M.; Stewart,G.; Ironside,J.W.; Cousens,S.N.; Smith,P.G. - Reporting of suspect new variant Creutzfeldt-Jakob disease - Lancet 1997 Mar 22; 349(9055): 847
AMYJ - Zeidler,M.; Collie,D.A.; Macleod,M.A.; Sellar,R.J.; Knight,R.S.G. - FLAIR MRI in sporadic Creutzfeldt-Jakob disease - Neurology 2001 Jan 23; 56(2): 282
AMYM - Zeidler,M.; Sellar,R.J.; Collie,D.A.; Knight,R.S.G.; Stewart,G.; Macleod,M.A.; Ironside,J.W.; Cousens,S.N.; Colchester,A.F.C.; Hadley,D.M.; Will,R.G. - The pulvinar sign on magnetic resonance imaging in variant Creutzfeldt-Jakob disease - Lancet 2000 Apr 22; 355(9213): 1412-8
AMYO - Zeidler,M.; Knight,R.S.G.; Stewart,G.; Ironside,J.W.; Will,R.G.; Green,A.J.E.; Pocchiari,M. - Diagnosis of Creutzfeldt-Jakob disease. Routine tonsil biopsy for diagnosis of new variant Creutzfeldt-Jakob disease is not justified. - British Medical Journal 1999 Feb 20; 318(7182): 538
AMZC - Zerr,I.; Pocchiari,M.; Collins,S.J.; Brandel,J.P.; de Pedro Cuesta,J.; Knight,R.S.G.; Bernheimer,H.; Cardone,F.; Delasnerie-Laupretre,N.; Cuadrado Corrales,N.; Ladogana,A.; Bodemer,M.; Fletcher,A.; Awan,T.; Ruiz Bremon,A.; Budka,H.; Laplanche,J.L.; Will,R.G.; Poser,S. - Analysis of EEG and CSF 14-3-3 proteins as aids to the diagnosis of Creutzfeldt-Jakob disease - Neurology 2000 Sep 26; 55(6): 811-5