NR ALHV
AU Szczudlik,A.; Slowik,A.
TI [Clinical presentations of spongiform encephalopathies in humans]
OT Obrazy kliniczne encefalopatii gabczastych u ludzi
QU Przeglad Lekarski 1999; 56(4): 324-6
PT journal article; review; review, tutorial
AB Spongiform encephalopathies (prion diseases) are a group of neurodegenerative disorders that affect both humans and animals and have common pathologic (spongiform changes, astrogliosis and neuronal loss) and clinical features. The paper shows clinical presentations of human spongioform encephalopathies: Creutzfeldt-Jakob disease, Gerstmann-Sträussler-Scheinker disease and fatal familiar insomnia. A new variant of Creutzfeldt-Jakob disease, with unique clinical (earlier onset, psychiatric symptoms and lack of the characteristic EEG abnormalities) and pathological features was described.
ZR 24
MH Animal; Creutzfeldt-Jakob Syndrome/diagnosis/pathology; Diagnosis, Differential; Electroencephalography; English Abstract; Gerstmann-Sträussler-Scheinker Disease/diagnosis; Human; Prion Diseases/classification/*diagnosis
AD Kliniki Neurologii Collgium Medicum Uniwersytetu Jagiellonskiego w Krakowie.
SP polnisch
PO Polen