NR AHPP
AU Lyketsos,C.G.; Kraus,M.
TI The dementia of Gerstmann-Sträussler-Scheinker syndrome: clinical variability demonstrated by two case reports.
QU Journal of Neuropsychiatry and Clinical Neurosciences 1995 Spring; 7(2): 239-42
PT journal article
AB Two cases of Gerstmann-Sträussler-Scheinker syndrome (GSS) are discussed in detail. These cases illustrate the variable clinical course and mostly cortical features of GSS-associated dementia. Given the availability of genetic tests that can now diagnose GSS, clinicians should consider these tests in cases where patients with dementia have extensive family histories or if the clinical course is atypical for Alzheimer's or vascular dementia.
ZR 9
MH Adult; Alzheimer Disease/diagnosis/psychology; Atrophy; Case Report; Cerebral Cortex/pathology; Dementia, Vascular/diagnosis/psychology; Diagnosis, Differential; Diagnostic Imaging; Female; Gerstmann-Sträussler-Scheinker Disease/*diagnosis/genetics/psychology; Human; Male; Middle Age; Neurologic Examination; Neuropsychological Tests
AD Neuropsychiatry and Memory Group, Johns Hopkins University School of Medicine, Baltimore, Maryland, USA
SP englisch
PO USA