NR AGZU
AU Lang,C.J.G.; Schüler,P.; Engelhardt,A.; Spring,A.; Brown,P.
TI Probable Creutzfeldt-Jakob disease after a cadaveric dural graft
QU European Journal of Epidemiology 1995 Feb; 11(1): 79-81
PT journal article
AB A 26-year old female who had received a cervical cadaveric dural graft 7 years earlier developed psychotic behavior and generalized myoclonic jerks. Following rapid deterioration and appearance of high-charge sharp periodic waves on electroencephalography she died within two months. We believe that this patient is the first German who acquired Creutzfeldt-Jakob disease by dural implant.
IN Eine 26-jährige Frau erkrankte 7 Jahre nach der Implantation fremder Hirnhaut anscheinend an der Creutzfeldt-Jakob-Krankheit und starb binnen 2 Monaten. Sie zeigte psyschotisches Verhalten, generelles Muskelzittern und scharfe periodische Hirnstromwellen. Dies scheint der erste Fall einer Übertragung der Creutzfeldt-Jakob-Krankheit durch ein Hirnhautimplantat in Deutschland zu sein.
ZR 0
MH Adult; Astrocytoma/surgery; Cadaver; Case Report; Creutzfeldt-Jakob Syndrome/etiology/*transmission; *Disease Transmission, Horizontal; Dura Mater/*transplantation; Electroencephalography; Fatal Outcome; Female; Human; Iatrogenic Disease; Reoperation; Spinal Cord Neoplasms/surgery; Tissue Transplantation/adverse effects
AD Neurologische Klinik der Friedrich-Alexander-Universität Erlangen-Nürnberg, Schwabachanlage 6, D-91054 Erlangen, Germany
SP englisch
PO Niederlande