NR AEIY
AU Galatioto,S.; De Luca,M.J.; Majorana,A.; Puglisi,R.M.; Gugliotta,M.A.; Distefano,G.
TI [Juvenile spongiform encephalopathy with unusual pathomorphologic findings]
OT Encefalopatia spongiforme giovanile con insoliti reperti patomorfologici
QU Rivista di Neurologia 1988 Nov-Dec; 58(6): 241-4
PT journal article
AB A 27-year-old man presented disturbances of gait and language, quickly followed by intellectual deterioration, tetraplegia, anarthria and myoclonus. Histological examination of a cerebral biopsy showed not only cortical changes consistent with the diagnosis of Creutzfeldt-Jakob disease, but also many amyloid-plaques with variable morphology. The diagnostic interpretation of the case particularly as to concern his relationship to s.c. Gerstmann-Sträussler syndrome is discussed.
MH Adult; Age Factors; Case Report; Creutzfeldt-Jakob Syndrome/complications/*pathology; English Abstract; Human; Male; Slow Virus Diseases/complications/*pathology
AD Istituto di Scienze Neurologiche e Neurochirurgiche dell'Universita di Messina.
SP italienisch
PO Italien