NR ABVN
AU Brown,P.; Gajdusek,D.C.
TI The human spongiform encephalopathies: kuru, Creutzfeldt-Jakob disease, and the Gerstmann-Sträussler-Scheinker syndrome.
QU Current Topics in Microbiology and Immunology 1991; 172: 1-20
PT journal article; review; review, academic
ZR 101
MH Adolescent; Adult; Amyloid/chemistry/genetics; Amyloid beta-Protein Precursor/chemistry/genetics; Animal; Cannibalism; *Creutzfeldt-Jakob; Syndrome/epidemiology/genetics/microbiology/pathology/transmission; Female; Food Contamination; Genes, Dominant; *Gerstmann-Sträussler-Scheinker; Disease/epidemiology/genetics/microbiology/pathology; Human; Iatrogenic Disease; Incidence; Infant; *Kuru/epidemiology/microbiology/pathology/transmission; Male; Middle Age; Mutation; Nerve Tissue Proteins/chemistry/genetics; New Guinea/epidemiology; PrPc Proteins; Prevalence; Primates/microbiology; Prions/chemistry/genetics; Protein Conformation; Protein Precursors/chemistry/genetics; Scrapie/transmission; Sheep/microbiology; Slow Virus Diseases/microbiology/transmission/veterinary; World Health
AD Paul Brown (pwb@codon.nih.gov), Laboratory of Central Nervous System Studies, National Institute of Neurological Disorders and Stroke, National Institutes of Health, Bethesda, MD 20892, USA
SP englisch
PO Deutschland