NR AAYO
AU Baniukiewicz,E.; Drozdowski,W.; Kulczycki,J.; Zimnoch,L.; Lechowicz,W.
TI [A sporadic case of Creutzfeldt-Jakob disease with peculiar neuropathological lesions]
OT Sporadyczny przypadek choroby Creutzfeldta-Jakoba o szczegolnym obrazie neuropatologicznym
QU Neurologia i Neurochirurgia Polska 1999 May-Jun; 33(3): 685-91
PT journal article
AB The authors report a case of Creutzfeldt-Jakob disease in a man aged 60 years from a family without a history of similar disease. The disease extended over 11 months. In the clinical picture initially equilibrium disturbances and dementia with psychotic symptoms predominated, EEG pattern was not typical of CJD. Neuropathological examination revealed extensive spongiform lesions in the cortex of all cerebral lobes, in striatum and substantia nigra, moreover a considerable number of kuru plaques was found in cerebellar cortex. The authors consider that the case meets the criteria accepted for the sporadic form of CJD but believe that the final differentiation from the Gerstmann-Streussler-Scheinker syndrome should be based on genetic studies.
MH Case Report; Cerebellum/pathology; Diagnosis, Differential; Electroencephalography; Electromyography; English Abstract; Extremities/physiopathology; Fatal Outcome; Human; Magnetic Resonance Imaging; Male; Middle Age; Occipital Lobe/*pathology
AD Kliniki Neurologii Akademii Medycznej w Bialymstoku.
SP polnisch
PO Polen