AFGV - Hegde,R.S.; Mastrianni,J.A.; Scott,M.R.D.; DeFea,K.A.; Tremblay,P.; Torchia,M.; DeArmond,S.J.; Prusiner,S.B.; Lingappa,V.R. - A transmembrane form of the prion protein in neurodegenerative disease - Science 1998 Feb 6; 279(5352): 827-34
ANRJ - Korth,C.; Kaneko,K.; Groth,D.; Heye,N.; Telling,G.; Mastrianni,J.A.; Parchi,P.; Gambetti,P.; Will,R.; Ironside,J.; Heinrich,C.; Tremblay,P.; DeArmond,S.J.; Prusiner,S.B. - Abbreviated incubation times for human prions in mice expressing a chimeric mouse-human prion protein transgene - Proceedings of the National Academy of Sciences of the United States of America 2003 Apr 15; 100(8): 4784-9
ATXD - Li,X.; Rowland,L.P.; Mitsumoto,H.; Przedborski,S.; Bird,T.D.; Schellenberg,G.D.; Peskind,E.; Johnson,N.; Siddique,T.; Mesulam,M.M.; Weintraub,S.; Mastrianni,J.A. - Prion protein codon 129 genotype prevalence is altered in primary progressive aphasia - Annals of Neurology 2005 Dec; 58(6): 858-64
AUNZ - Liebman,S.W.; Mastrianni,J.A. - Tracking the elusive prion - Trends in Molecular Medicine 2005 Oct; 11(10): 439-41
AHQS - MacGowan,D.J.; Delanty,N.; Petito,F.; Edgar,M.; Mastrianni,J.A.; DeArmond,S.J. - Isolated myoclonic alien hand as the sole presentation of pathologically established Creutzfeldt-Jakob disease: a report of two patients. - Journal of Neurology, Neurosurgery and Psychiatry 1997 Sep; 63(3): 404-7
APJT - Mastrianni,J.A.; Roos,R.P. - Wrinkles and folds of the prion protein - Neurology 2003 Nov 11; 61(9): 1168-9
AIAJ - Mastrianni,J.A.; Roos,R.P. - "Out, damned spot! out, I say!...": issues related to prion decontamination. - Neurology 2002 Aug 27; 59(4): 488-9
AIAK - Mastrianni,J.A.; Capellari,S.; Telling,G.C.; Han,D.; Bosque,P.J.; Prusiner,S.B.; DeArmond,S.J. - Inherited prion disease caused by the V210I mutation: transmission to transgenic mice. - Neurology 2001 Dec 26; 57(12): 2198-205
AIAL - Mastrianni,J.A.; Roos,R.P. - The prion diseases - Seminars in Neurology 2000; 20(3): 337-52
AIAM - Mastrianni,J.A.; Nixon,R.; Layzer,R.; Telling,G.C.; Han,D.; DeArmond,S.J.; Prusiner,S.B. - Prion protein conformation in a patient with sporadic fatal insomnia - The New England Journal of Medicine 1999 May 27; 340(21): 1630-8
AIAN - Mastrianni,J.A. - The prion diseases: Creutzfeldt-Jakob, Gerstmann-Sträussler-Scheinker, and related disorders. - Journal of Geriatric Psychiatry and Neurology 1998 Summer; 11(2): 78-97
ASCZ - Mastrianni,J.A.; Nixon,R.; Layzer,R.; DeArmond,S.J.; Prusiner,S.B. - Fatal sporadic insomnia (FSI) - fatal familial insomnia (FFI) phenotype without a mutation of the prion protein (PrP) gene - Neurology 1997; 48(N3): 5036
AIAO - Mastrianni,J.A.; Iannicola,C.; Myers,R.M.; DeArmond,S.J.; Prusiner,S.B. - Mutation of the prion protein gene at codon 208 in familial Creutzfeldt-Jakob disease - Neurology 1996 Nov; 47(5): 1305-12
AQGF - Mastrianni,J.A.; Prusiner,S.B. - The prevalence of heritable prion disease is underestimated by clinical-assessment - Neurology 1996; 46(N2): 4098
AIAP - Mastrianni,J.A.; Curtis,M.T.; Oberholtzer,J.C.; Da Costa,M.M.; DeArmond,S.J.; Prusiner,S.B.; Garbern,J.Y. - Prion disease (PrP-A117V) presenting with ataxia instead of dementia - Neurology 1995 Nov; 45(11): 2042-50
ASDA - Mastrianni,J.A.; Iannicola,C.; Myers,R.; Prusiner,S.B. - Identification of a new mutation of the prion protein gene at codon-208 in a patient with Creutzfeldt-Jakob-disease - Neurology 1995; 45(4): A 201-201
AQRI - Nixon,R.R.; Mastrianni,J.A.; Roberts,J.; Prusiner,S.B.; DeArmond,S.J. - Sporadic occurrence of fatal thalamic insomnia without a prion protein gene mutation - Journal of Neuropathology and Experimental Neurology 1996; 55(N5): 661 Nr. 225
AWSF - Norstrom,E.M.; Ciaccio,M.F.; Rassbach,B.; Wollmann,R.; Mastrianni,J.A. - Cytosolic prion protein toxicity is independent of cellular prion protein expression and prion propagation - Journal of Virology 2007 Mar; 81(6): 2831-7
AVBQ - Norstrom,E.M.; Mastrianni,J.A. - The charge structure of helix 1 in the prion protein regulates conversion to pathogenic PrPsc - Journal of Virology 2006 Sep; 80(17): 8521-9
ASXL - Norstrom,E.M.; Mastrianni,J.A. - The AGAAAAGA palindrome in PrP is required to generate a productive PrPsc-PrPc complex that leads to prion propagation - The Journal of Biological Chemistry 2005 Jul 22; 280(29): 27236-43
AJGI - Patry,D.; Curry,B.; Easton,D.; Mastrianni,J.A.; Hogan,D.B. - Creutzfeldt-Jakob disease (CJD) after blood product transfusion from a donor with CJD - Neurology 1998 Jun; 50(6): 1872-3
ALCC - Spudich,S.; Mastrianni,J.A.; Wrensch,M.; Gabizon,R.; Meiner,Z.; Kahana,I.; Rosenmann,H.; Kahana,E.; Prusiner,S.B. - Complete penetrance of Creutzfeldt-Jakob disease in Libyan Jews carrying the E200K mutation in the prion protein gene - Molecular Medicine 1995 Sep; 1(6): 607-13
ALPJ - Telling,G.C.; Parchi,P.; DeArmond,S.J.; Cortelli,P.; Montagna,P.; Gabizon,R.; Mastrianni,J.A.; Lugaresi,E.; Gambetti,P.; Prusiner,S.B. - Evidence for the conformation of the pathologic isoform of the prion protein enciphering and propagating prion diversity - Science 1996 Dec 20; 274(5295): 2079-82
ARWU - Telling,G.C.; Mastrianni,J.A.; DeArmond,S.J.; Prusiner,S.B. - Exploring mechanisms of prion propagation using mice expressing human and chimeric mouse-human prion protein transgenes - Neurology 1996; 46(N2): 3085
ALPL - Telling,G.C.; Scott,M.R.D.; Mastrianni,J.A.; Gabizon,R.; Torchia,M.; Cohen,F.E.; DeArmond,S.J.; Prusiner,S.B. - Prion propagation in mice expressing human and chimeric PrP transgenes implicates the interaction of cellular PrP with another protein - Cell 1995 Oct 6; 83(1): 79-90
AMSU - Worrall,B.B.; Rowland,L.P.; Chin,S.S.M.; Mastrianni,J.A. - Amyotrophy in prion diseases - Archives of Neurology 2000 Jan; 57(1): 33-8
ARYF - Yang,S.L.; Mastrianni,J.A.; DeArmond,S.J. - Neuropathological changes colocalize with deposition of PrPcJD and loss of PrPc in Creutzfeldt-Jakob-disease - Journal of Neuropathology and Experimental Neurology 1996; 55(N5): 636 Nr. 123