AIAP - Mastrianni,J.A.; Curtis,M.T.; Oberholtzer,J.C.; Da Costa,M.M.; DeArmond,S.J.; Prusiner,S.B.; Garbern,J.Y. - Prion disease (PrP-A117V) presenting with ataxia instead of dementia - Neurology 1995 Nov; 45(11): 2042-50
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